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颅咽管瘤是起源于原始口腔外胚层行成的颅咽管残余上皮细胞,占全部脑肿瘤的2.5%-4%,是常见的颅内先天肿瘤。半数为儿童发病。肿瘤多数为囊性或部分囊性。囊内含有大量胆固醇结晶。
\n好发部位:鞍上,可向下丘脑、鞍旁、鞍内、第三脑室、额底、脚间池、桥小脑角等部位发展。
\n临床表现:1.视力、视野障碍;2.内分泌紊乱 发育迟缓、易于倦怠、食欲不振、面色苍白、性器官发育不良、停经、泌乳、体温异常、意识和睡眠障碍、尿崩、肥胖、精神障碍;3.头痛、呕吐等脑积水、颅高压症状4.局部神经功能障碍(肿瘤部位相关)。
\n影像学检查:1.CT可见环状(蛋壳杨)钙化;2.MRI可见鞍上占位。
\n治疗:1.开颅手术;2.立体定向囊液抽吸+32P内放射+伽马刀放射治疗。
\n术前、术后头颅核磁对比:术前头颅核磁红色箭头所示高信号(白色)为肿瘤;术后头颅核磁绿色箭头所示高信号(白色)为术腔
\n\n
术前、术后头颅CT对比:术前头颅CT红色箭头所示高信号(白色)为肿瘤钙化部分,术后头颅CT红色箭头所示肿瘤钙化部分消失。肿瘤全切除。
\n转自:海军总医院官网
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